Scoliosis is the medical term for curvature of the spine. In diseases of the muscles and nerves, curvature of the spine occurs because the muscles on either side of the spine are weak. They are not working effectively to hold the spine straight. Once significant scoliosis has developed, it will worsen unless surgery is performed. Braces and special seating are not usually effective in preventing progression of the problem.
Complications of Scoliosis
1. Pain and Discomfort-
When the spine curves, ligaments and other tissues are stretched. This causes backache, discomfort and pain and difficulty sitting for long periods of time. Eventually the patient is unable to sit without discomfort and may become bedridden.
2. Impairment of Breathing -
If the spine curves too much, the rib cage is deformed and this in turn deforms the lungs. Breathing becomes less efficient.
What Can Be Done About Scoliosis?
A number of operations have been devised to overcome the effects of progressive scoliosis. During the operation, the spine is straightened out as much as possible and metal rods are placed on each side of the spine to keep the spine straight. These metal rods prevent the spine from curving again.
What Are The Risks Of The Operation?
Operations for scoliosis are major procedures. They do carry some risk as follows.
1. Haemorrhage : This can be dealt with by the surgeon before the operation is finished.
2. Wound breakdown or infection : These are very uncommon and can be treated with antibiotics.
3. Damage to the spinal cord : Although the nervous tissue of the spinal cord is not touched at the time of the operation, straightening out the spine can sometimes lead to pressure on the nervous tissue or cause the blood supply to the nervous tissue to be impaired. Paralysis of the legs, impairment of sensation in the legs and impairment of bladder function are possible resulting problems but these are rare.
4. Anaesthetic problems : Although the operation takes several hours, the risks of the anaesthetic itself are no greater for this operation than for other equivalent operations.
5. Post-operative respiratory failure : Most patients with muscle and nerve disease having this operation have significantly poor breathing capacity before the operation. This is because of weakness of the muscles of the chest wall. Often the child's ability to cough is also very poor. These factors, along with poor chest movement due to discomfort in the days immediately following the operation, can make children susceptible to chest infection which even further affects breathing capacity.
Occasionally it is necessary for the patient to be in the intensive care unit for a few days following the operation. Sometimes the patients breathing requires assistance by a mechanical ventilator. Very rarely, if post operative chest problems are severe and prolonged, the patient's chest muscles becomes weaker than they were before the operation and it becomes difficult for the patient to breath by him or herself again. It should be stressed that this is a rare but nevertheless serious problem.
Implications Of Not Having The Spinal Surgery
Risks Versus Benefits
After surgery, almost all families have been pleased that the decision was made to proceed, despite that decision having been a difficult one. The children themselves comment that they feel better about themselves and about how they look when they are sitting straighter in their chair. Some mobility of the trunk is lost because of the rods holding the spine straight but this is usually not a major problem.
What Can You Do?
Additional Information Available
- Related DMD Information
- Physiotherapy for DMD
- DMD - A Guide For Parents.A comprhensive 50 page book.
History | Logo | MD Centre | Mission | Partmerships | Policies | Employment | Calendar | Clinical | Glossary | Links | Duchenne | ED | FSH | LGD | Myotonic | Mitochondrial | SMA | Newsletters | Genetics | InfoMD | PEG | 101 | Physio | Recreation | Resources | Respiratory | Scoliosis | Media | Ryan's Cafe | CampMDA | ChallengeMD | Forum | NMDRC | Wheelie's Rest | Programs | Futures | Respite | CINRG | Glossary | Clinics | Bequests | Donations | Fundraising | InMemory | MDAngels | Volunteers | Workplace Giving